Asymptomatic Left Ventricular Malignant Psammomatous Melanotic Schwannoma
Asymptomatic Left Ventricular Malignant Psammomatous Melanotic Schwannoma
C. Laurin,J. Claveau,3 Authors,J. Perron
TLDR
The challenges with the diagnosis of MPMS are discussed, the rationale of the treatment strategy is explained, and the rationale for the diagnosis and treatment strategy are explained in this first report ofMPMS involving the left heart ventricle.
Abstract
Malignant psammomatous melanotic schwannoma (MPMS) is a rare type of tumour, occasionally reported to occur with mediastinal involvement. Histopathologic similarities with melanoma may lead to a wrong diagnosis, but distinguishing between types of tumours is mandatory for adequate management and prognosis. MPMS may be aggressive and manifest unpredictable behavior, with a poor midterm prognosis despite benign histopathologic features. We discuss the challenges that come with a diagnosis of MPMS, and the rationale for our treatment strategy, in this first report regarding MPMS involving the left heart ventricle.