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A case of rapid avacopan-induced liver injury in pediatric granulomatosis with polyangiitis.

T. Nishino,Shinya Tomori,2 Authors,M. Mimaki

2024 · DOI: 10.1007/s00467-024-06376-8
Pediatric nephrology (Berlin, West) · 4 Citations

TLDR

Children with anti-neutrophil cytoplasmic antibody-associated vasculitis benefit immensely from avacopan as it reduces the requirement for steroids, but the dosage and follow-up intervals are unclear.

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