147 LONG TERM MANAGEMENT PROBLEMS IN CARNITINE DEFICIENT CARDIOMYOPATHY
147 LONG TERM MANAGEMENT PROBLEMS IN CARNITINE DEFICIENT CARDIOMYOPATHY
M. Tripp,A. Shug,R. Arcilla
1985 · DOI: 10.1203/00006450-198504000-00177
Pediatric Research · 1 Citations
TLDR
Two patients with SCD and CCM, treated for 4 and 2½ years with L-carnitine, had syncope with sinus node dysfunction; both now take C, 150 mg/kg/d to maintain plasma C, and both had normal EF at these times.
